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KMID : 0356620110260030258
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Journal of Korean Society of Endocrinology
2011 Volume.26 No. 3 p.258 ~ p.262
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Case Reports and Estimated Prevalence of Adrenal Pheochromocytoma in Patients with Neurofibromatosis Type I in Korea
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Jung Ju-Yang
Ahn Seun-Joo
Yoon Hyung-Young
Chung Yoon-Sok
Ko Jung-Min
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Abstract
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We report three patients with adrenal pheochromocytoma who were associated with type I neurofibromatosis. Two of them were asymptomatic, but one case involved hypertension. We reviewed medical records and adrenal imaging, and estimated the prevalence of adrenal pheochromocytoma among neurofibromatosis type I patients in one university hospital in Korea. A total of 658 patients were coded for neurofibromatosis type I (Q85.0 with International Classification of Diseases 10 version) with clinical impression, but only 371 were confirmed via 1997 National Institute of Health criteria. Adrenal images were generated in 203 patients, and 3 of them were diagnosed with pheochromocytoma. According to the results of this study, the estimated prevalence of adrenal pheochromocytoma in type I neurofibromatosis was 0.30-1.48%.
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KEYWORD
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Neurofibromatosis type I, Pheochromocytoma, Prevalence
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